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Trial details imported from ClinicalTrials.gov

For full trial details, please see the original record at https://clinicaltrials.gov/study/NCT07169279




Registration number
NCT07169279
Ethics application status
Date submitted
23/06/2025
Date registered
11/09/2025
Date last updated
11/09/2025

Titles & IDs
Public title
Interventional Study of Infigratinib in Children < 3 Years Old With Achondroplasia (ACH)
Scientific title
Phase 2b, Randomized, Double-Blind, Placebo-Controlled Clinical Trial, Preceded by a Single Ascending Dose Portion and a Phase 2 Open-Label Portion, to Evaluate the Safety and Efficacy of Oral Infigratinib in Infants and Young Children With Achondroplasia
Secondary ID [1] 0 0
QBGJ398-204
Universal Trial Number (UTN)
Trial acronym
Linked study record

Health condition
Health condition(s) or problem(s) studied:
Achondroplasia 0 0
Condition category
Condition code
Human Genetics and Inherited Disorders 0 0 0 0
Other human genetics and inherited disorders
Musculoskeletal 0 0 0 0
Other muscular and skeletal disorders
Metabolic and Endocrine 0 0 0 0
Other metabolic disorders
Metabolic and Endocrine 0 0 0 0
Other endocrine disorders

Intervention/exposure
Study type
Interventional
Description of intervention(s) / exposure
Treatment: Drugs - Infigratinib is provided as a single dose of minitablets for oral administration
Treatment: Drugs - Infigratinib is provided as sprinkle capsules for daily oral administration
Treatment: Drugs - Infigratinib or placebo comparator is provided as sprinkle capsules for daily oral administration
Treatment: Drugs - Infigratinib is provided as sprinkle capsules for daily oral administration

Experimental: SAD Cohort 1 infigratinib (2 to less than 3 years old) - Single Ascending Dose Escalation and PK Portion

Experimental: SAD Cohort 2 infigratinib (1 to less than 2 years old) - Single Ascending Dose Escalation and PK Portion

Experimental: SAD Cohort 3 infigratinib (6 months to less than 1 year old) - Single Ascending Dose Escalation and PK Portion

Experimental: SAD Cohort 4 infigratinib (0 to less than 6 months old) - Single Ascending Dose Escalation and PK Portion

Experimental: Phase 2 Cohort 1 infigratinib (2 to less than 3 years old) - Open-label Safety and PK Portion

Experimental: Phase 2 Cohort 2 infigratinib (1 to less than 2 years old) - Open-label Safety and PK Portion

Experimental: Phase 2 Cohort 3 infigratinib (6 months to less than 1 year old) - Open-label Safety and PK Portion

Experimental: Phase 2 Cohort 4 infigratinib (0 to less than 6 months) - Open-label Safety and PK Portion

Experimental: Phase 2B Cohort 1 infigratinib (2 to less than 3 years old) - Randomized Safety and Efficacy Portion

Experimental: Phase 2B Cohort 2 infigratinib (6 months to less than 2 years old) - Randomized Safety and Efficacy Portion

Experimental: Phase 2B Cohort 3 infigratinib (0 to less than 6 months old) - Randomized Safety and Efficacy Portion

Experimental: Open- label Extension infigratinib (0 months to 3 years [+6 months old]) - Open-label extension portion continuing to assess safety and efficacy in children until they reach 3 years old (+6 months)

Placebo comparator: Phase 2B Cohort 1 Placebo (2 to less than 3 years old) - Randomized Safety and Efficacy study

Placebo comparator: Phase 2B Cohort 2 placebo (6 months to less than 2 years old) - Randomized Safety and Efficacy study

Placebo comparator: Phase 2B Cohort 3 Placebo (0 to less than 6 months old) - Randomized Safety and Efficacy study


Treatment: Drugs: Infigratinib is provided as a single dose of minitablets for oral administration
* The initial cohort dose of infigratinib will begin at the protocol-specified starting dose, with subsequent cohort escalation based on protocol specific criteria.
* The target dose is the dose that will provide similar exposure to the dose of 0.25 mg/kg/day in participants 3 years old and older.
* The dose and number of minitablets will be calculated based on individual participant age and weight.

Treatment: Drugs: Infigratinib is provided as sprinkle capsules for daily oral administration
* The cohort dose of infigratinib will be the dose identified in the Single Ascending Dose portion for the age group.
* The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months.

Treatment: Drugs: Infigratinib or placebo comparator is provided as sprinkle capsules for daily oral administration
* The cohort dose of infigratinib or placebo will be the dose confirmed in the Phase 2 portion for the age group.
* The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months.

Treatment: Drugs: Infigratinib is provided as sprinkle capsules for daily oral administration
* The dose of infigratinib will be the dose confirmed in the Phase 2 portion and used in the Phase 2b portion for the age group.
* The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months for the first year and every 6 months thereafter.

Intervention code [1] 0 0
Treatment: Drugs
Comparator / control treatment
Control group

Outcomes
Primary outcome [1] 0 0
Single Ascending Dose Portion: Identify the dose of infigratinib to be used in each age cohort of the Phase 2 potion of the study (by assessing safety and PK of infigratinib and its active metabolites)
Timepoint [1] 0 0
2 weeks
Primary outcome [2] 0 0
Phase 2 Portion: Confirm the doses to be used in each age cohort in the Phase 2b portion of the study (by assessing safety and PK of infigratinib and its active metabolites).
Timepoint [2] 0 0
52 weeks
Primary outcome [3] 0 0
Phase 2b Portion: Evaluate the safety and efficacy of infigratinib in infants and children < 3 years old with ACH (by assessing AE's & SAE's)
Timepoint [3] 0 0
52 weeks
Primary outcome [4] 0 0
Extension Portion: Evaluate the safety and efficacy of infigratinib in participants who completed the Phase 2 or Phase 2b portion of the study until they have reached 3 years old (+6 months) (by assessing AE's and SAE's)
Timepoint [4] 0 0
3 years and 6 months
Secondary outcome [1] 0 0
Phase 2: Evaluate the safety of oral daily doses of infigratinib (by assessing AEs and SAEs)
Timepoint [1] 0 0
52 weeks
Secondary outcome [2] 0 0
Phase 2: Evaluate changes in indicators of growth (by assessing change from BL in body length z-score at Week 52 in relation to ACH tables)
Timepoint [2] 0 0
52 weeks
Secondary outcome [3] 0 0
Phase 2: Evaluate changes in indicators of body proportions (by assessing change from BL to Week 52 in upper-to-lower body segment ratio and head circumference/body length ratio)
Timepoint [3] 0 0
52 weeks
Secondary outcome [4] 0 0
Phase 2: Change from BL in Health-related Quality of Life (HRQoL) (as assessed by Infant and Toddler Quality of Life Inventory [ITQoL] tool)
Timepoint [4] 0 0
52 weeks
Secondary outcome [5] 0 0
Phase 2: Milestone Development of motor skills (assessed with development milestone charts)
Timepoint [5] 0 0
52 weeks
Secondary outcome [6] 0 0
Phase 2: Milestone Development of language skills (assessed with development milestone charts)
Timepoint [6] 0 0
52 weeks
Secondary outcome [7] 0 0
Phase 2: Milestone Development of personal-social skills (assessed with development milestone charts)
Timepoint [7] 0 0
52 weeks
Secondary outcome [8] 0 0
Phase 2: Skull and brain morphology (as assessed using MRI)
Timepoint [8] 0 0
52 weeks
Secondary outcome [9] 0 0
Phase 2: Age at closure of cranial structures (as assessed by physical examination)
Timepoint [9] 0 0
52 weeks
Secondary outcome [10] 0 0
Phase 2: Age at closure of fontanelles (as assessed by physical examination)
Timepoint [10] 0 0
52 weeks
Secondary outcome [11] 0 0
Phase 2: Incidence of surgical interventions (i.e., cervical decompression, adenotonsillectomy etc)
Timepoint [11] 0 0
52 weeks
Secondary outcome [12] 0 0
Phase 2: Incidence and severity of sleep apnea (as assessed by polysomnography)
Timepoint [12] 0 0
52 weeks
Secondary outcome [13] 0 0
Phase 2: Bone morphology (as assessed using x-rays)
Timepoint [13] 0 0
52 weeks
Secondary outcome [14] 0 0
Phase 2b: Evaluate the pharmacokinetic (PK) profile of infigratinib and its metabolites (by assessing the PK of infigratinib and its active metabolites)
Timepoint [14] 0 0
52 weeks
Secondary outcome [15] 0 0
Phase 2b: Change from BL in Health-related Quality of Life (HRQoL) (as assessed by Infant and Toddler Quality of Life Inventory [ITQoL] tool)
Timepoint [15] 0 0
52 weeks
Secondary outcome [16] 0 0
Phase 2b: Evaluate the safety of oral daily doses of infigratinib (by assessing AEs and SAEs)
Timepoint [16] 0 0
52 weeks
Secondary outcome [17] 0 0
Phase 2b: Evaluate changes in indicators of growth (by assessing change from BL in body length z-score at Week 52 in relation to ACH tables)
Timepoint [17] 0 0
52 weeks
Secondary outcome [18] 0 0
Phase 2b: Evaluate changes in indicators of body proportions (by assessing change from BL to Week 52 in upper-to-lower body segment ratio and head circumference/body length ratio)
Timepoint [18] 0 0
52 weeks
Secondary outcome [19] 0 0
Phase 2b: Milestone Development of motor skills (assessed with development milestone charts)
Timepoint [19] 0 0
52 weeks
Secondary outcome [20] 0 0
Phase 2b: Milestone development of language skills (assessed with development milestone charts)
Timepoint [20] 0 0
52 weeks
Secondary outcome [21] 0 0
Phase 2b: Milestone development of personal-social skills (assessed with development milestone charts)
Timepoint [21] 0 0
52 weeks
Secondary outcome [22] 0 0
Phase 2b: Skull and brain morphology (as assessed using MRI)
Timepoint [22] 0 0
52 weeks
Secondary outcome [23] 0 0
Phase 2b: Age at closure of cranial structures (as assessed by physical examination)
Timepoint [23] 0 0
52 weeks
Secondary outcome [24] 0 0
Phase 2b: Age at closure of fontanelles (as assessed by physical examination)
Timepoint [24] 0 0
52 weeks
Secondary outcome [25] 0 0
Phase 2b: Incidence of surgical interventions (i.e., cervical decompression, adenotonsillectomy etc)
Timepoint [25] 0 0
52 weeks
Secondary outcome [26] 0 0
Phase 2b: Incidence and severity of sleep apnea (as assessed by polysomnography)
Timepoint [26] 0 0
52 weeks
Secondary outcome [27] 0 0
Phase 2b: Bone morphology (as assessed using x-rays)
Timepoint [27] 0 0
52 weeks
Secondary outcome [28] 0 0
Extension Phase: Evaluate the safety of oral daily doses of infigratinib (by assessing AEs and SAEs)
Timepoint [28] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [29] 0 0
Extension Phase: Change from BL in body length Z-score
Timepoint [29] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [30] 0 0
Extension Phase: Change from BL in upper to lower body segment ratio (cm)
Timepoint [30] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [31] 0 0
Extension Phase: Change from BL in head circumference body length ratio
Timepoint [31] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [32] 0 0
Extension Phase: Milestone development of social/emotional skills (assessed with development milestone charts)
Timepoint [32] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [33] 0 0
Extension Phase: Milestone development of language communication skills (assessed with development milestone charts)
Timepoint [33] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [34] 0 0
Extension Phase: Milestone development of cognitive skills (assessed with development milestone charts)
Timepoint [34] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [35] 0 0
Extension Phase: Milestone development of movement/physical development skills (assessed with development milestone charts)
Timepoint [35] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [36] 0 0
Extension Phase: Age at closure of cranial structures (as assessed by physical examination)
Timepoint [36] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [37] 0 0
Extension Phase: Age at closure of fontanelles (as assessed by physical examination)
Timepoint [37] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [38] 0 0
Extension Phase: Incidence of surgical interventions (i.e., cervical decompression, adenotonsillectomy etc)
Timepoint [38] 0 0
Until they have reached 3 years old (+6 months)
Secondary outcome [39] 0 0
Extension Phase: Bone morphology (as assessed using x-rays)
Timepoint [39] 0 0
Until they have reached 3 years old (+6 months)

Eligibility
Key inclusion criteria
* Diagnosis of ACH confirmed by genetic testing. If prospective participants had prior genetic testing, the diagnosis must be confirmed by a report from a certified laboratory, documenting the specific mutation.
* Age 0 to 32 months (2 years and 8 months) at screening.
* Signed informed consent, which must be obtained from each participant's parent(s) or legal guardian.
* Parent(s)/Guardian(s) willing and able to attend all study visits and comply with all study requirements.
* Parent(s)/Guardian(s) willing and able to comply with the routine care of the study participants according to local guidance for the management of infants and young children with ACH.
* Able to swallow age-appropriate oral medication.
* In participants <1 year old, be compliant with recommended vitamin D supplementation of 5 10 µg/day or higher (or as recommended by country specific guidelines).
Minimum age
0 Years
Maximum age
32 Months
Sex
Both males and females
Can healthy volunteers participate?
No
Key exclusion criteria
* Participants who have hypochondroplasia or diagnosis of genetic condition other than ACH, or any clinical condition that can affect growth.
* Gestational age at birth <37 weeks and/or birth weight <2500 grams.
* Gastroesophageal reflux disease requiring prolonged treatment (>1 week) with prohibited medications.
* Evidence of cervicomedullary compression, as defined by an Achondroplasia Foramen Magnum Score (AFMS) 4, symptomatic or asymptomatic, diagnosed during MRI done at screening or a previous MRI done at any time if the participant had not undergone decompression surgery.
* History of fracture of a long bone or spine within 6 months prior to screening.
* Any other significant concurrent disease or condition that, in the view of the investigator and/or sponsor, would confound assessment of efficacy or safety of infigratinib and/or would require treatment with a prohibited medication (per protocol), and/or would place the participant at high risk for poor treatment compliance or for failure to complete the study.
* Regular long-term (>3 weeks; more than twice/year) treatment with supraphysiologic doses of glucocorticoid therapy (ie, >15 mg/m2/day of hydrocortisone or equivalent) or treatment with glucocorticoids at anti-inflammatory doses (for over 3 weeks within 6 months of the screening visit. NOTE: Low-dose topical, inhaled, or intranasal corticosteroids are acceptable.
* Significant abnormality in screening laboratory results,
* Allergy or hypersensitivity to any components of the study drug.

Study design
Purpose of the study
Treatment
Allocation to intervention
Randomised controlled trial
Procedure for enrolling a subject and allocating the treatment (allocation concealment procedures)
Methods used to generate the sequence in which subjects will be randomised (sequence generation)
Masking / blinding
Blinded (masking used)
Who is / are masked / blinded?
The people receiving the treatment/s


The people analysing the results/data
Intervention assignment
Parallel
Other design features
Phase
Phase 2
Type of endpoint/s
Statistical methods / analysis

Recruitment
Recruitment status
Not yet recruiting
Data analysis
Reason for early stopping/withdrawal
Other reasons
Date of first participant enrolment
Anticipated
Actual
Date of last participant enrolment
Anticipated
Actual
Date of last data collection
Anticipated
Actual
Sample size
Target
Accrual to date
Final
Recruitment in Australia
Recruitment state(s)
VIC
Recruitment hospital [1] 0 0
Murdoch Children's Research Institute - Parkville
Recruitment postcode(s) [1] 0 0
3052 - Parkville
Recruitment outside Australia
Country [1] 0 0
United States of America
State/province [1] 0 0
California
Country [2] 0 0
United States of America
State/province [2] 0 0
Maryland
Country [3] 0 0
United States of America
State/province [3] 0 0
Wisconsin
Country [4] 0 0
Canada
State/province [4] 0 0
Ontario
Country [5] 0 0
Canada
State/province [5] 0 0
Quebec
Country [6] 0 0
Norway
State/province [6] 0 0
Oslo
Country [7] 0 0
Singapore
State/province [7] 0 0
Singapore
Country [8] 0 0
Spain
State/province [8] 0 0
Vitoria-Gasteiz
Country [9] 0 0
United Kingdom
State/province [9] 0 0
Glasgow
Country [10] 0 0
United Kingdom
State/province [10] 0 0
London
Country [11] 0 0
United Kingdom
State/province [11] 0 0
Manchester
Country [12] 0 0
United Kingdom
State/province [12] 0 0
Sheffield

Funding & Sponsors
Primary sponsor type
Commercial sector/industry
Name
QED Therapeutics, Inc., a Bridgebio company
Address
Country

Ethics approval
Ethics application status

Summary
Brief summary
Trial website
Trial related presentations / publications
Public notes

Contacts
Principal investigator
Name 0 0
Address 0 0
Country 0 0
Phone 0 0
Fax 0 0
Email 0 0
Contact person for public queries
Name 0 0
QED Therapeutics Inc.
Address 0 0
Country 0 0
Phone 0 0
18772805655
Fax 0 0
Email 0 0
Contact person for scientific queries

Data sharing statement
Will individual participant data (IPD) for this trial be available (including data dictionaries)?
No
No/undecided IPD sharing reason/comment


What supporting documents are/will be available?

No Supporting Document Provided


Results publications and other study-related documents

No documents have been uploaded by study researchers.